敞 开 心 扉心扉升主动脉右心室左心室左冠瓣右冠瓣无冠瓣主动脉瓣 Aortic Valve主 动 脉 瓣 狭 窄x 号选手Aortic Stenosis目录CONTENTS 定义病因学临床表现诊断 主动脉瓣狭窄是由于先天性或后天性因素致主动脉瓣病变导致其在收缩期不能完全开放。定义 Definition病因学 Etiology65%25%10%65%25%10%退行性风湿性先天性50%>50 yraortic valve calcification10%>80 yrSuffer ASSudden Cardiac Death10%症状 SymptomNormal无症状期Asymptomatic StageAS缺血淤血心排量容量负荷心绞痛angina晕厥syncope呼吸困难dyspnea首发症状心绞痛 anginaNORMALAS心排量耗氧量冠状动脉功能性缺血晕厥 syncope心排量脑组织缺血心律失常头臂干左颈总动脉冠状动脉50%呼吸困难 dyspnea左心衰竭肺淤血劳力性呼吸困难左心室左心房肺无症状期症状发作死亡事件生存率50%die in first 2 years生存时间杂音 Murmur 声音是由物体振动产生,通过介质传播并能被人或动物听觉器官所感知的波动现象。湍流杂音 MurmurNormalAS主动脉瓣听诊区主动脉瓣听诊区收缩期喷射样杂音,向颈部传导,可及震颤超声心动图 Echocardiography右室流出道右心房左心房三尖瓣肺动脉后背右左前胸NormalAS• 病史与症状诊断 Diagnosis • 典型心脏杂音• 超声心动图Normal3.0-4.0cm2Mild AS>1.5cm2Moderate AS1.0-1.5cm2Severe AS<1.0cm2分度 GraduationREPAIRREPLACESUMMARY333symptometiologygraduation课后思考1试从病理生理学机制解释:主动脉瓣狭窄的预后为什么会与“三联征”的出现顺序相关 ?2主动脉瓣狭窄需要与哪些疾病鉴别?参考文献[1] 杨跃进. 经导管主动脉瓣置入术的现状及展望[J]. 中国循环杂志, 2013(03):161-163.[2] Carabello B A, Paulus W J. Aortic stenosis[J]. Lancet, 2009,373(9667):956-966.[3] Iung B, Baron G, Butchart E G, et al. A prospective survey of patients with valvular heart disease in Europe: The Euro Heart Survey on Valvular Heart Disease[J]. Eur Heart J, 2003,24(13):1231-1243.[4] Nishimura R A, Otto C M, Bonow R O, et al. 2014 AHA/ACC guideline for the management of patients with valvular heart disease: a report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines[J]. J Thorac Cardiovasc Surg, 2014,148(1):e1-e132.感谢聆听X 号选手